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Standard Text: Select all that apply.1. “There may be genetic concerns that should be discussed with the physician.”2. “Your children will not be affected by the disease.”3. “The disease is passed only through the mother’s blood line.”4. “Each child will have a 50% chance of inheriting the gene.”5. “There is a strong chance that your children will be carriers, but they will only develop the disease if their mother is also a carrier.”Correct Answer: 1,4Rationale 1: Huntington’s disease is a genetic disorder. Further discussion and information are necessary.Rationale 2: Children have a 50% chance of inheriting the disease.Rationale 3: Either sex can transmit and inherit Huntington’s disease.Rationale 4: The chance that a child will inherit the disorder is 50%.Rationale 5: Persons who inherit this faulty gene will develop the disorder. There is no carrier state.Global Rationale: Cognitive Level: ApplyingClient Need: Health Promotion and MaintenanceClient Need Sub: Nursing/Integrated Concepts: Nursing Process: ImplementationLearning Outcome: 23-1Question 7Type: MCSAThe nurse is caring for a patient with amyotrophic lateral sclerosis (ALS). The nurse plans care based on which understanding of the patient’s prognosis?1. The disease progresses slowly and is fatal.2. The disease will progress over many years but the patient’s quality of life will be good.3. The disease progresses rapidly but can be halted by drug therapy.4. The disease will progress slowly and can be controlled by medication.
Correct Answer: 1Rationale 1: The disease is slowly progressive and fatal and is characterized by weakness and wasting of muscles under voluntary control.Rationale 2: Quality of life is profoundly affected by this disorder.Rationale 3: Riluzole (Rilutek) is available to treat the disease, but it does not halt it. Death usually occurs due to respiratory failure.Rationale 4: The disease is slowly progressive and cannot be controlled by medication.Global Rationale: Cognitive Level: ApplyingClient Need: Physiological IntegrityClient Need Sub: Physiological AdaptationNursing/Integrated Concepts: Nursing Process: PlanningLearning Outcome: 23-3Question 8Type: MCSAOnce amyotrophic lateral sclerosis (ALS) is diagnosed, what is the priority nursing activity?1. Support the patient and family to meet physical and psychosocial needs.2. Monitor for infection.3. Assist the patient to avoid complications.4. Assist the patient to adapt to the disease.Correct Answer: 1Rationale 1: Support for the patient and family should receive the highest priority for nursing intervention.Rationale 2: It is important to monitor for infection, but this is not the most important intervention.Rationale 3: It is important to assist the patient and family to avoid complications, but this is not the most important intervention.